Table 1

Delphi 2 Responses in order of descending number of votes

PROBLEM
TREATMENT
VOTES

Systemic onset juvenile rheumatoid arthritis
Anti-IL-6 receptor antibody
62
Uveitis (juvenile rheumatoid arthritis, sarcoid, or idiopathic) unresponsive to methotrexate
Infliximab
50
Pediatric systemic lupus erythematosus
Mycophenolate mofetil
48
Thrombocytopenia unresponsive to standard therapy in systemic lupus erythematosus
Rituximab
47
Juvenile dermatomyositis unresponsive to prednisone and disease-modifying anti-rheumatic drugs
Enbrel
43
Systemic onset juvenile rheumatoid arthritis
Thalidomide
43
Systemic onset juvenile rheumatoid arthritis
Anakinra
36
Localized scleroderma
Combination: steroids and methotrexate
35
Juvenile dermatomyositis unresponsive to prednisone and disease-modifying anti-rheumatic drugs
Infliximab
29
Rash of juvenile dermatomyositis
Topical tacrolimus
27
Systemic lupus erythematosus proliferative nephritis unresponsive to pulse cyclophosphamide and mycophenolate mofetil
Combination: pulse cyclophosphamide and mycophenolate mofetil
25
Chronic Recurrent Multifocal Osteomyelitis that is not controlled by non-steroid anti-inflammatory drugs and/or that requires corticosteroids
Bisphosphonates
24
Localized scleroderma
Methotrexate orally
20
Linear scleroderma refractory to oral or subcutaneous methotrexate treatment
Oral mycophenolate mofetil treatment
19
Henoch Scholein Purpura
Glucocorticoid treatment
18
Osteoporosis
Alendronate and other possibilities
18
Pauciarticular juvenile rheumatoid arthritis
Intraarticular steroids
17
Systemic onset juvenile rheumatoid arthritis
Combination:TNF blockers and thalidomide
17
Behcet's
Infliximab
16
Early polyarticular juvenile rheumatoid arthritis
CTLA4-1g
16
Macrophage activation syndrome
Combination: cyclosporin + corticosteroids
15
Sarcoid arthritis
Enbrel
15
Severe systemic lupus erythematosus – cyclophosphamide dependent or resistant
Intravenous fludarabine
15
Rash of systemic lupus erythematosus
Topical tacrolimus
14
Acute rheumatic fever
Naproxen
13
Henoch Scholein Purpura with abdominal pain
Glucocorticoid treatment
13
Juvenile rheumatoid arthritis-temporomandibular joint arthritis
Corticosteroid joint injections
13
Systemic onset juvenile rheumatoid arthritis
Oral intravenous immunoglobulin as adjuvant therapy
10
Familial Mediterranean fever not responsive to colchicine
Anakinra
8
Refractory iritis in juvenile rheumatoid arthritis
Cyclosporin
8
Osteoporosis
Vitamin D – the various preparations
7
Raynaud's 10 and 20
Biofeedback
7
Familial Mediterranean fever
Anti-Interleukin 1
5
Systemic onset juvenile rheumatoid arthritis
Combination: hydroxychloroquine and standard therapy
2
Systemic onset juvenile rheumatoid arthritis
Combination: thalidomide and cyclosporin
2

Ota et al. Pediatric Rheumatology 2008 6:5   doi:10.1186/1546-0096-6-5