Idiopathic sclerosing mesenteritis in paediatrics: Report of a successfully treated case and a review of literature
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* Corresponding author: Kevin J Murray kevin.murray@health.wa.gov.au
Department of Pediatric Rheumatology, Princess Margaret Hospital for Children, Perth, WA, Australia
Pediatric Rheumatology 2010, 8:5 doi:10.1186/1546-0096-8-5
Published: 21 January 2010Abstract
A 6 year old female with symptoms of small bowel obstruction underwent an exploratory laparotomy which revealed widespread evidence of inflammatory fibrotic adhesions involving the jejunal mesentery. In view of persistent growth failure, chronic anaemia, elevated acute phase reactants and imaging evidence of a diffuse progressive inflammatory process, the child was treated with corticosteroids and methotrexate with complete response. The literature on juvenile idiopathic sclerosing mesenteritis has been reviewed.